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Anti-ALDH5A1/SSADH 兔多克隆抗体
¥1900
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货号: K1341439-100
预测分子量: 56 kDa
观测分子量: 54 kDa
别名: ALDH5A1, SSADH, SSDH, Aldehyde dehydrogenase family 5 member A1, NAD(+)-dependent succinic semialdehyde dehydrogenase
应用 | 种属
WB H
产品信息
蛋白质全称 线粒体琥珀酸半醛脱氢酶
别名 ALDH5A1, SSADH, SSDH, Aldehyde dehydrogenase family 5 member A1, NAD(+)-dependent succinic semialdehyde dehydrogenase
Uniprot ID Q8BWF0
免疫原 KLH偶联的小鼠ALDH5A1合成肽
抗体亚型 IgG
纯化方式 亲和纯化
预测分子量./观测分子量. 56 kDa / 54 kDa
应用
WB 免疫印迹
物种:人
稀释比:1: 500-1: 1000
阳性样品:
背景
This protein belongs to the aldehyde dehydrogenase family of proteins. This gene encodes a mitochondrial NAD(+)-dependent succinic semialdehyde dehydrogenase. A deficiency of this enzyme, known as 4-hydroxybutyricaciduria, is a rare inborn error in the metabolism of the neurotransmitter 4-aminobutyric acid (GABA). In response to the defect, physiologic fluids from patients accumulate GHB, a compound with numerous neuromodulatory properties. Two transcript variants encoding distinct isoforms have been identified for this gene.
储存条件
储存条件:储存条件在:-20℃下储存一年, 避免反复冻融.
储存缓冲液:含0.15% ProClin300防腐剂, 100 μg/mL牛血清白蛋白和50%甘油的磷酸盐缓冲液.
图像
ALDH5A1_WB
ALDH5A1_WB

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